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產(chǎn)品詳情
  • 產(chǎn)品名稱(chēng):Anti-IDUA抗體

  • 產(chǎn)品型號(hào):α-L-艾杜糖苷酶抗體
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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簡(jiǎn)單介紹:
Anti-IDUA抗體產(chǎn)品質(zhì)量穩(wěn)定,實(shí)驗(yàn)效果明顯,貨期快,價(jià)格優(yōu)惠,歡迎垂詢(xún)訂購(gòu)!我公司長(zhǎng)期供應(yīng)**組化抗體、WB抗體、**組化試劑盒和抗體試驗(yàn)所需全部相關(guān)試劑、熒光標(biāo)記抗體、單克隆抗體、多克隆抗體、各種標(biāo)記的二抗IgG/IgM/IgD/IgA等科研實(shí)驗(yàn)抗體。Anti-IDUA抗體用于**組化實(shí)驗(yàn),WB實(shí)驗(yàn),相應(yīng)的標(biāo)記抗體有HRP標(biāo)記抗體,FITC標(biāo)記,BIO等。
詳情介紹:
Rabbit  Anti-IDUA
Cat. Number:
Anti-IDUA抗體KL-15542R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan Anti-IDUA抗體sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008].
Also known as:
IDUA_HUMAN; Alpha-L-iduronidase;Anti-IDUA抗體 IDA; Iduronidase alpha L; MPS1.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Horse, .
Immunogen: KLH conjugated synthetic peptide derived from human IDUA.
Predicted Molecular Weight: 70kDa.Anti-IDUA抗體
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-IDUA抗體
Optimal working dilutions must be determined by the end user.
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