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產品詳情
  • 產品名稱:Anti-DUX4抗體

  • 產品型號:雙同源框蛋白4抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-DUX4抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-DUX4抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-DUX4
Cat. Number:
Anti-DUX4抗體KL-12369R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
DUX4 is a homeodomainAnti-DUX4抗體 protein with a similar protein sequence to Pax3 and Pax7. Defects in DUX4 may be the cause of facioscapulohumeral muscular dystrophy (FSHD). FSHD is characterized by weakness of the muscles of the face, upper-arm and shoulder girdle. Severity is highly variable. Weakness is slowly progressive and about 20% of affected individuals eventually require a wheelchair. Approximately 70-90% of individuals have inherited the disease-causing deletion from a parent, and approximately 10-30% of affected individuals have FSHD as the result of a de novo deletion. Offsprings of an affected individual have a 50% chance of inheriting the deletion.
Also known as:
Double homeobox protein Anti-DUX4抗體10; Double homeobox protein 4; Double homeobox protein 4/10; DUX10; DUX4_HUMAN.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, .
Immunogen: KLH conjugated synthetic peptide derived from human DUX4.
Predicted Molecular Weight:Anti-DUX4抗體 45kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-DUX4抗體
Optimal working dilutions must be determined by the end user.
kl513Hu01 煙堿型膽堿受體β2(CHRNβ2)多克隆抗體 Polyclonal Antibody to Cholinergic Receptor, Nicotinic, Beta 2 (CHRNb2)
kl514Hu01 白介素1受體關聯激酶1(IRAK1)多克隆抗體 Polyclonal Antibody to Interleukin 1 Receptor Associated Kinase 1 (IRAK1)
kl516Hu01 凸素1(PROM1)多克隆抗體 Polyclonal Antibody to Prominin 1 (PROM1)
kl517Hu01 顆粒溶素(GNLY)多克隆抗體 Polyclonal Antibody to Granulysin (GNLY)
kl518Hu01 白介素1受體關聯激酶4(IRAK4)多克隆抗體 Polyclonal Antibody to Interleukin 1 Receptor Associated Kinase 4 (IRAK4)
kl520Hu01 白介素1受體關聯激酶3(IRAK3)多克隆抗體 Polyclonal Antibody to Interleukin 1 Receptor Associated Kinase 3 (IRAK3)
kl521Hu01 黏膜地址素細胞黏附分子(MAdCAM1)多克隆抗體 Polyclonal Antibody to Mucosal Addressin Cell Adhesion Molecule 1 (MAdCAM1)
kl522Hu01 肺部激活調節趨化因子(klC)多克隆抗體 Polyclonal Antibody to Pulmonary Activation Regulated Chemokine (klC)
kl523Mu01 趨化因子C-X3-C-基元受體1(CX3CR1)多克隆抗體 Polyclonal Antibody to Chemokine C-X3-C-Motif Receptor 1 (CX3CR1)
kl524Hu01 神經元凋亡抑制蛋白(NAIP)多克隆抗體 Polyclonal Antibody to Neuronal Apoptosis Inhibitory Protein (NAIP)
kl530Hu01 血小板膜糖蛋白Ⅳ(GP4)多克隆抗體 Polyclonal Antibody to Platelet Membrane Glycoprotein IV (GP4)
kl532Hu01 維甲酸誘導基因1蛋白(RIG1)多克隆抗體 Polyclonal Antibody to Retinoic Acid Inducible Gene 1 Protein (RIG1)
kl533Hu01 基質金屬蛋白酶16(MMP16)多克隆抗體 Polyclonal Antibody to Matrix Metalloproteinase 16 (MMP16)
kl537Hu01 絲氨酸蛋白酶2(PRSS2)多克隆抗體 Polyclonal Antibody to Protease, Serine 2 (PRSS2)
kl538Hu01 細胞胱硫醚γ裂解酶(CSE)多克隆抗體 Polyclonal Antibody to Cystathionine Gamma Lyase (CSE)
kl538Ra01 細胞胱硫醚γ裂解酶(CSE)多克隆抗體 Polyclonal Antibody to Cystathionine Gamma Lyase (CSE)
kl539Hu01 血清淀粉樣P物質(SAP)多克隆抗體 Polyclonal Antibody to Serum Amyloid P Component (SAP)
kl539Mu01 血清淀粉樣P物質(SAP)多克隆抗體 Polyclonal Antibody to Serum Amyloid P Component (SAP)

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