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產品詳情
  • 產品名稱:Anti-C16orf57抗體

  • 產品型號:16號染色體開放閱讀框57抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-C16orf57抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-C16orf57抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-C16orf57
Cat. Number:
Anti-C16orf57抗體KL-9631R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Involvement in disease;Defects in C16orf57 are the cause of poikiloderma with neutropenia (PN). PN is a genodermatosis characterized by poikiloderma, pachyonychia and chronic neutropenia. The disorder starts as a papular erythematous rash on the limbs during the first year of life. It gradually spreads centripetally and, Anti-C16orf57抗體as the papular rash resolves, hypo- and hyperpigmentation result, with development of telangiectasias. Another skin manifestation is pachyonychia, but alopecia and leukoplakia are distinctively absent. One of the most important extracutaneous symptoms is an increased susceptibility to infections, mainly affecting the respiratory system, primarily due to a chronic neutropenia and to neutrophil functional defects. Bone marrow abnormalities account for neutropenia and may evolve into myelodysplasia associated with the risk of leukemic transformation. Poikiloderma with neutropenia shows phenotypic overlap with Rothmund-Thomson syndrome.
Also known as:
Chromosome 16 open reading frame 57; Anti-C16orf57抗體CP057_HUMAN; FLJ13154; UPF0406 protein C16orf57.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human C16orf57.
Predicted Molecular Anti-C16orf57抗體Weight: 30kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working Anti-C16orf57抗體dilutions must be determined by the end user.
kl011Mu02 Runt相關轉錄因子2(RUNX2)多克隆抗體 Polyclonal Antibody to Runt Related Transcription Factor 2 (RUNX2)
kl016Mu01 血小板膜糖蛋白Ⅰbβ多肽(GP2Bβ)多克隆抗體 Polyclonal Antibody to Glycoprotein Ib Beta Polypeptide, Platelet (GP1Bb)
kl016Mu02 血小板膜糖蛋白Ⅰbβ多肽(GP2Bβ)多克隆抗體 Polyclonal Antibody to Glycoprotein Ib Beta Polypeptide, Platelet (GP1Bb)
kl019Mu02 血管生成素樣蛋白4(ANGPTL4)多克隆抗體 Polyclonal Antibody to Angiopoietin Like Protein 4 (ANGPTL4)
kl021Mu02 連環蛋白β1(CTNNβ1)多克隆抗體 Polyclonal Antibody to Catenin Beta 1 (CTNNb1)
kl023Bo01 β-乳球蛋白(βLg)多克隆抗體 Polyclonal Antibody to Beta-Lactoglobulin (bLg)
kl024Mu01 趨化因子C-C-基元受體10(CCR10)多克隆抗體 Polyclonal Antibody to Chemokine C-C-Motif Receptor 10 (CCR10)
kl024Mu02 趨化因子C-C-基元受體10(CCR10)多克隆抗體 Polyclonal Antibody to Chemokine C-C-Motif Receptor 10 (CCR10)
kl025Ra01 神經介素U(NMU)多克隆抗體 Polyclonal Antibody to Neuromedin U (NMU)
kl028Ca01 白蛋白(ALB)多克隆抗體 Polyclonal Antibody to Albumin (ALB)
kl028Mu02 白蛋白(ALB)多克隆抗體 Polyclonal Antibody to Albumin (ALB)
kl029Hu01 整合素α2B(ITGα2B)多克隆抗體 Polyclonal Antibody to Integrin Alpha 2B (ITGa2B)
kl034Mu02 粘蛋白4(MUC4)多克隆抗體 Polyclonal Antibody to Mucin 4 (MUC4)
kl036Mu02 生長**受體(GHR)多克隆抗體 Polyclonal Antibody to Growth Hormone Receptor (GHR)
kl038Mu01 谷氨酸半胱氨酸連接酶(GCLM)多克隆抗體 Polyclonal Antibody to Glutamate Cysteine Ligase, Modifier Subunit (GCLM)
kl038Mu02 谷氨酸半胱氨酸連接酶(GCLM)多克隆抗體 Polyclonal Antibody to Glutamate Cysteine Ligase, Modifier Subunit (GCLM)
kl038Ra01 谷氨酸半胱氨酸連接酶(GCLM)多克隆抗體 Polyclonal Antibody to Glutamate Cysteine Ligase, Modifier Subunit (GCLM)
kl040Mu02 波形蛋白(VIM)多克隆抗體 Polyclonal Antibody to Vimentin (VIM)
kl041Mu01 玻連蛋白(VTN)多克隆抗體 Polyclonal Antibody to Vitronectin (VTN)
kl041Mu02 玻連蛋白(VTN)多克隆抗體 Polyclonal Antibody to Vitronectin (VTN)

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