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產品詳情
  • 產品名稱:Anti-CDMP1抗體

  • 產品型號:軟骨衍生形態發生蛋白1/GDF 5抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-CDMP1抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-CDMP1抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-CDMP1
Cat. Number:
Anti-CDMP1抗體KL-6580R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Defects in GDF5 are the cause of acromesomelic chondrodysplasia Grebe type (AMDG) . Acromesomelic chondrodysplasias are rare hereditary skeletal disorders characterized by short stature, very short limbs, Anti-CDMP1抗體and hand/foot malformations. The severity of limb abnormalities increases from proximal to distal with profoundly affected hands and feet showing brachydactyly and/or rudimentary fingers (knob-like fingers). AMDG is an autosomal recessive form characterized by normal axial skeletons and missing or fused skeletal elements within the hands and feet. Defects in GDF5 are the cause of acromesomelic chondrodysplasia Hunter-Thompson type (AMDH). AMDH is an autosomal recessive form of dwarfism. Patients have limb abnormalities, with the middle and distal segments being most affected and the lower limbs more affected than the upper. AMDH is characterized by normal axial skeletons and missing or fused skeletal elements within the hands and feet. Defects in GDF5 are the cause of brachydactyly type C (BDC). BDC is an autosomal dominant disorder characterized by an abnormal shortness of the fingers and toes.
Also known as:
Cartilage derived morphogeneticAnti-CDMP1抗體 protein 1; Cartilage-derived morphogenetic protein 1; CDMP-1; CDMP1; GDF-5; Gdf 5; GDF5_HUMAN; Growth differentiation factor 5; Growth/differentiation factor 5; LAP4; Radotermin.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, .
Immunogen: KLH conjugated synthetic peptide derived from human CDMP1/GDF5.
Predicted Molecular Weight: 55kDa.
Storage:
Shipped at 4℃, Store at -20℃Anti-CDMP1抗體 (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions Anti-CDMP1抗體must be determined by the end user.
kl893Mu02 血管內皮生長因子受體3(VEGFR3)多克隆抗體 Polyclonal Antibody to Vascular Endothelial Growth Factor Receptor 3 (VEGFR3)
kl942Mu01 前-B-**細胞基因1(VPREB1)多克隆抗體 Polyclonal Antibody to Pre-B-Lymphocyte Gene 1 (VPREB1)
kl021Po01 重肽鐵蛋白(FTH)多克隆抗體 Polyclonal Antibody to Ferritin, Heavy Polypeptide (FTH)
kl838Po01 抑制素βA(INHβA)多克隆抗體 Polyclonal Antibody to Inhibin Beta A (INHbA)
kl065Ra01 丙氨酸氨肽酶(AAP)多克隆抗體 Polyclonal Antibody to Alanine Aminopeptidase (AAP)
kl018Ra01 α-乳清蛋白(αLA)多克隆抗體 Polyclonal Antibody to Alpha-Lactalbumin (aLA)
kl172Ra01 CD1d分子(CD1d)多克隆抗體 Polyclonal Antibody to Cluster Of Differentiation 1d (CD1d)
kl113Ra01 生長分化因子11(GDF11)多克隆抗體 Polyclonal Antibody to Growth Differentiation Factor 11 (GDF11)
kl198Ra01 88kDa核孔蛋白(NUP88)多克隆抗體 Polyclonal Antibody to Nucleoporin 88kDa (NUP88)
kl523Ra01 血小板衍生生長因子AA(PDGFAA)多克隆抗體 Polyclonal Antibody to Platelet Derived Growth Factor AA (PDGFAA)
kl273Ra01 孕酮受體(PGR)多克隆抗體 Polyclonal Antibody to Progesterone Receptor (PGR)
kl316Ra01 X-射線修復交叉互補蛋白6(XRCC6)多克隆抗體 Polyclonal Antibody to X-Ray Repair Cross Complementing 6 (XRCC6)
kl087Eq01 單核細胞趨化蛋白1(MCP1)多克隆抗體 Polyclonal Antibody to Monocyte Chemotactic Protein 1 (MCP1)
kl599Hu51 顆粒酶A(GZMA)多克隆抗體 Polyclonal Antibody to Granzyme A (GZMA)
kl150Hu04 癌胚抗原(CEA)多克隆抗體 Polyclonal Antibody to Carcinoembryonic Antigen (CEA)
kl769Hu02 肝脂酶(LIPC)多克隆抗體 Polyclonal Antibody to Likle, Heklic (LIPC)
kl132Hu02 脂聯素受體2(ADIPOR2)多克隆抗體 Polyclonal Antibody to Adiponectin Receptor 2 (ADIPOR2)
kl593Ra03 肌原纖蛋白1(FBN1)多克隆抗體 Polyclonal Antibody to Fibrillin 1 (FBN1)

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