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產品詳情
  • 產品名稱:Anti-BBS9抗體

  • 產品型號:巴爾得-別德爾綜合征相關蛋白9抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-BBS9抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-BBS9抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-BBS9
Cat. Number:
Anti-BBS9抗體KL-11511R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
BBS9 is an 887 amino Anti-BBS9抗體acid protein that localizes to both the cytoplasm and the centrosome and exists as six alternatively spliced isoforms. Expressed in a wide variety of tissues, including liver, lung, heart, brain and skeletal muscle, BBS9 functions as a component of the multi-protein BBSome complex which is required for ciliogenesis and is regulated by GDP/GTP exchange factors. Defects in the gene encoding BBS9 are associated with the pathogenesis of Bardet-Biedl syndrome type 9 (BBS9), an autosomal recessive disorder that is characterized by severe pigmentary retinopathy, early onset obesity, polydactyly, hypogenitalism, renal malformation and mental retardation. Additionally, chromosomal aberrations involving the BBS9 gene may play a role in the formation of Wilms tumor 5 (WT5).Anti-BBS9抗體
Also known as:
B1 antibody; Bardet Biedl syndrome 9; Bardet-Biedl syndrome 9 protein; bbs9; C18 antibody D1 antibody MGC118917; 1 Anti-BBS9抗體gene protein; Protein PTHB1; PTH-responsive osteosarcoma B1 protein; PTHB1; PTHB1_HUMAN.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Pig, Horse, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human BBS9.
Predicted Molecular Weight: 99kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-BBS9抗體
Optimal working dilutions must be determined by the end user.
kl531Mu01 纖溶酶原激活物抑制因子2(PAI2)多克隆抗體 Polyclonal Antibody to Plasminogen Activator Inhibitor 2 (PAI2)
kl531Ra01 纖溶酶原激活物抑制因子2(PAI2)多克隆抗體 Polyclonal Antibody to Plasminogen Activator Inhibitor 2 (PAI2)
kl531Rb51 纖溶酶原激活物抑制因子2(PAI2)多克隆抗體 Polyclonal Antibody to Plasminogen Activator Inhibitor 2 (PAI2)
kl532Hu01 纖溶酶原激活物抑制因子1(PAI1)多克隆抗體 Polyclonal Antibody to Plasminogen Activator Inhibitor 1 (PAI1)
kl532Mu01 纖溶酶原激活物抑制因子1(PAI1)多克隆抗體 Polyclonal Antibody to Plasminogen Activator Inhibitor 1 (PAI1)
kl532Ra01 纖溶酶原激活物抑制因子1(PAI1)多克隆抗體 Polyclonal Antibody to Plasminogen Activator Inhibitor 1 (PAI1)
kl532Rb51 纖溶酶原激活物抑制因子1(PAI1)多克隆抗體 Polyclonal Antibody to Plasminogen Activator Inhibitor 1 (PAI1)
kl532Si01 纖溶酶原激活物抑制因子1(PAI1)多克隆抗體 Polyclonal Antibody to Plasminogen Activator Inhibitor 1 (PAI1)
kl533Hu01 細胞間粘附分子3(ICAM3)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 3 (ICAM3)
kl534Hu01 細胞間粘附分子2(ICAM2)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 2 (ICAM2)
kl534Mu01 細胞間粘附分子2(ICAM2)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 2 (ICAM2)
kl534Rb51 細胞間粘附分子2(ICAM2)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 2 (ICAM2)
kl536Hu01 亮氨酰氨基肽酶(LAP)多克隆抗體 Polyclonal Antibody to Leucine Aminopeptidase (LAP)
kl536Ra01 亮氨酰氨基肽酶(LAP)多克隆抗體 Polyclonal Antibody to Leucine Aminopeptidase (LAP)
kl537Hu01 神經元特異性烯醇化酶(NSE)多克隆抗體 Polyclonal Antibody to Enolase, Neuron Specific (NSE)
kl537Mu01 神經元特異性烯醇化酶(NSE)多克隆抗體 Polyclonal Antibody to Enolase, Neuron Specific (NSE)

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