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產品詳情
  • 產品名稱:Anti-APRT抗體

  • 產品型號:腺嘌呤磷酸核糖轉移酶抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-APRT抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-APRT抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-APRT
Cat. Number:
Anti-APRT抗體KL-12506R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
APRT is a 180 amino acid protein that localizes to the cytoplasm and belongs to the purine/pyrimidine phosphoribosyltransferase family. Existing as a homodimer, APRT functions to catalyze the Anti-APRT抗體formation of inorganic pyrophosphate and AMP from adenine and 5-phosphoribosyl-1-pyrophosphate (PRPP), a reaction that is essential for both purine metabolism and AMP biosynthesis. Defects in the gene encoding APRT are the cause of APRT deficiency, also known as 2,8-dihydroxyadenine urolithiasis, which is an autosomal recessive disease that results in renal failure. The gene encoding APRT maps to human chromosome 16, which encodes over 900 genes and comprises nearly 3% of the human genome. The GAN gene is located on chromosome 16 and, with mutation, may lead to giant axonal neuropathy, a nervous system disorder characterized by increasing malfunction with growth. The rare disorder Rubinstein-Taybi syndrome is also associated with chromosome 16, as is Crohn's disease, which is a gastrointestinal inflammatory condition.
Also known as:
Anti-APRT抗體Adenine phosphoribosyltransferase; AMP; AMP diphosphorylase; AMP pyrophosphorylase; APRT; APT_HUMAN; DKFZp686D13177; MGC125856; MGC125857; MGC129961; Transphosphoribosidase.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human APRT.
Predicted Molecular Weight: 19kDa.
Storage:
Shipped at 4℃, Anti-APRT抗體Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Anti-APRT抗體Optimal working dilutions must be determined by the end user.
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kl329Hu01 性別決定區Y框蛋白9(SOX9)多克隆抗體 Polyclonal Antibody to Sex Determining Region Y Box Protein 9 (SOX9)
kl342Hu01 色氨酸羥化酶1(TPH1)多克隆抗體 Polyclonal Antibody to Tryptophan Hydroxylase 1 (TPH1)
kl342Ra01 色氨酸羥化酶1(TPH1)多克隆抗體 Polyclonal Antibody to Tryptophan Hydroxylase 1 (TPH1)
kl343Hu01 色氨酸羥化酶2(TPH2)多克隆抗體 Polyclonal Antibody to Tryptophan Hydroxylase 2 (TPH2)
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kl371Mu01 鈉/鉀離子轉運ATP酶β1肽(ATP1β1)多克隆抗體 Polyclonal Antibody to ATkle, Na+/K+ Transporting Beta 1 Polypeptide (ATP1b1)
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kl374Mu01 鈣離子轉運ATP酶A2(ATP2A2)多克隆抗體 Polyclonal Antibody to ATkle, Ca++ Transporting, Cardiac Muscle, Slow Twitch 2 (ATP2A2)
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