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產(chǎn)品詳情
  • 產(chǎn)品名稱:Anti-Aprataxin抗體

  • 產(chǎn)品型號:共濟失調(diào)性眼球運動功能喪失相關蛋白AOA1抗體
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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簡單介紹:
Anti-Aprataxin抗體產(chǎn)品質(zhì)量穩(wěn)定,實驗效果明顯,貨期快,價格優(yōu)惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-Aprataxin抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-Aprataxin
Cat. Number:
Anti-Aprataxin抗體KL-12504R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Aprataxin is a nuclear protein, present in both the nucleoplasm and the nucleolus, which is a member of the histidine triad (HIT) superfamily. Aprataxin is involved in DNA single-strand break repair, mediating protein-protein interactions with molecules responding to DNA damage. Aprataxin contains three Anti-Aprataxin抗體conserved domains: an N-terminal forkhead-associated (FHA) domain which mediates protein-protein interactions, a HIT domain that is similar to Hint, and a C-terminal zinc finger domain. Loss of function mutations in APTX, the gene encoding for Aprataxin, destabilize the Aprataxin protein and result in a rare neurological disorder known as ataxia-oculomotor apraxia, characterized by abnormal movements of the head and eyes. These mutations either target the HIT domain or truncate the protein N-terminal to a zinc finger.
Also known as:
Anti-Aprataxin抗體AOA 1; AOA; AOA; AOA1; AOA1; Aprataxin; Aprataxin; Aprataxin homolog; APTX; APTX; APTX_HUMAN; Ataxia 1 early onset with hypoalbuminemia; Ataxia 1 early onset with hypoalbuminemia; Ataxia1 early onset with hypoalbuminemia; AXA 1; AXA1; AXA1; EAOH; EAOH; EOAHA; EOAHA; FHA HIT; FHA HIT; FHA-HIT; FLJ20157; FLJ20157; Forkhead associated domain histidine triad like; Forkhead associated domain histidine triad like; Forkhead associated domain histidine triad like protein; Forkhead-associated domain histidine triad-like protein; MGC1072; MGC1072.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts Anti-Aprataxin抗體with: Human, Mouse, Rat, Horse, Rabbit, .
Immunogen: KLH conjugated synthetic peptide derived from human AOA1/Aprataxin.
Predicted Molecular Weight: 41kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
IHC-P=1:100-500  IHC-F=1:100-500   
Not yet tested in other applications. 
Anti-Aprataxin抗體Optimal working dilutions must be determined by the end user.
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kl039Ra01 組胺H3受體(HRH3)多克隆抗體 Polyclonal Antibody to Histamine Receptor H3 (HRH3)
kl040Hu01 組胺H4受體(HRH4)多克隆抗體 Polyclonal Antibody to Histamine Receptor H4 (HRH4)
kl040Mu01 組胺H4受體(HRH4)多克隆抗體 Polyclonal Antibody to Histamine Receptor H4 (HRH4)
kl043Hu01 腎上腺髓質(zhì)素受體(AMR)多克隆抗體 Polyclonal Antibody to Adrenomedullin Receptor (AMR)
kl045Hu01 G蛋白偶聯(lián)雌**受體1(GPER)多克隆抗體 Polyclonal Antibody to G Protein Coupled Estrogen Receptor 1 (GPER)
kl077Hu01 嘌呤能受體P2X7(P2RX7)多克隆抗體 Polyclonal Antibody to Purinergic Receptor P2X, Ligand Gated Ion Channel 7 (P2RX7)
kl122Hu01 淀粉樣蛋白β前體樣蛋白2(APLP2)多克隆抗體 Polyclonal Antibody to Amyloid Beta Precursor Like Protein 2 (APLP2)
kl150Hu01 組氨酸豐富鈣結(jié)合蛋白(HRC)多克隆抗體 Polyclonal Antibody to Histidine Rich Calcium Binding Protein (HRC)
kl151Hu01 天冬氨酸β羥化酶(ASPH)多克隆抗體 Polyclonal Antibody to Askltate Beta Hydroxylase (ASPH)
kl152Hu01 小泛素相關修飾蛋白2(SUMO2)多克隆抗體 Polyclonal Antibody to Small Ubiquitin Related Modifier Protein 2 (SUMO2)
kl168Mu01 Discs大同源物4(DLG4)多克隆抗體 Polyclonal Antibody to Discs, Large Homolog 4 (DLG4)
kl168Ra01 Discs大同源物4(DLG4)多克隆抗體 Polyclonal Antibody to Discs, Large Homolog 4 (DLG4)
kl183Hu01 胞質(zhì)分裂作用因子3(DOCK3)多克隆抗體 Polyclonal Antibody to Dedicator Of Cytokinesis 3 (DOCK3)
kl186Mu01 Podocan蛋白(PODN)多克隆抗體 Polyclonal Antibody to Podocan (PODN)
kl187Hu01 酮戊二酸脫氫酶(OGDH)多克隆抗體 Polyclonal Antibody to Oxoglutarate Dehydrogenase (OGDH)

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