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產品詳情
  • 產品名稱:Anti-HEXB chain B抗體

  • 產品型號:Beta氨基己糖苷酶beta亞基蛋白B鏈抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-HEXB chain B抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-HEXB chain B抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-HEXB chain B
Cat. Number:
Anti-HEXB chain B抗體KL-15468R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Hexosaminidase B is the beta subunit of the lysosomal enzyme beta-hexosaminidase that, together with the cofactor GM2 activator protein, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Beta-hexosaminidase is composed of two subunits, alpha and beta, which are Anti-HEXB chain B抗體encoded by separate genes. Both beta-hexosaminidase alpha and beta subunits are members of family 20 of glycosyl hydrolases. Mutations in the alpha or beta subunit genes lead to an accumulation of GM2 ganglioside in neurons and neurodegenerative disorders termed the GM2 gangliosidoses. Beta subunit gene mutations lead to Sandhoff disease (GM2-gangliosidosis type II). [provided by RefSeq, Jul 2008].
Also known as:
Beta hexosaminidase beta chain; Beta hexosaminidase subunit beta; Beta N acetylhexosaminidase; Beta-hexosaminidase subunit beta Anti-HEXB chain B抗體chain B; Beta-N-acetylhexosaminidase subunit beta; Cervical cancer proto oncogene 7 protein; Cervical cancer proto-oncogene 7 protein; ENC 1AS; HCC 7; HCC-7; HCC7; HEX B; Hexb; HEXB_HUMAN; Hexosaminidase B (beta polypeptide); Hexosaminidase B; Hexosaminidase subunit B; HexosaminidaseB; N acetyl beta glucosaminidase; N-acetyl-beta-glucosaminidase subunit beta; HEXB chain B.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Cow, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human HEXB.
Predicted Molecular Weight: 22/50kDa.Anti-HEXB chain B抗體
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   Anti-HEXB chain B抗體
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.
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kl046Ra01 S100鈣結合蛋白A10(S100A10)多克隆抗體 Polyclonal Antibody to S100 Calcium Binding Protein A10 (S100A10)
kl050Ra01 高遷移率族AT Hook蛋白1(HMGA1)多克隆抗體 Polyclonal Antibody to High Mobility Group AT Hook Protein 1 (HMGA1)
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kl130Ga01 頭蛋白(NOG)多克隆抗體 Polyclonal Antibody to Noggin (NOG)
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