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產品詳情
  • 產品名稱:Anti-Hamartin抗體

  • 產品型號:錯構素蛋白抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-Hamartin抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-Hamartin抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-Hamartin
Cat. Number:
Anti-Hamartin抗體KL-15406R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Tuberous sclerosis complex (TSC) is an autosomal dominant genetic disorder characterized by mental retardation and the widespread development of distinctive tumors termed hamartomas. Two different genetic loci have Anti-Hamartin抗體been linked to TSC; one of these loci, the tuberous sclerosis-2 gene (TSC2), encodes a protein called tuberin and the other loci, tuberous sclerosis-1 gene (TSC1), encodes a protein called hamartin. Tuberin and hamartin interact with each other forming a cystoplasmic complex. Hamartin interacts with the ezrin-radixin-moesin (ERM) family of actin-binding proteins and inhibition of hamartin activity results in loss of cell adhesion. Hamartin is present in most ***** tissues with strong expression in brain, heart, and kidney.
Also known as:
Hamartin; kiaa0243; LAM; TSC; TSC1; Anti-Hamartin抗體Tsc1 gene; TSC1_HUMAN; Tuberous sclerosis 1; Tuberous sclerosis 1 protein.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, .
Immunogen: KLH conjugated synthetic peptide derived from human Hamartin.
Predicted Molecular Weight: 130kDa.Anti-Hamartin抗體
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   Anti-Hamartin抗體
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.
kl674Hu01 補體成分1s(C1s)多克隆抗體 Polyclonal Antibody to Complement Component 1, S Subcomponent (C1s)
kl677Hu01 黑素轉鐵蛋白(MFI2)多克隆抗體 Polyclonal Antibody to Melanotransferrin (MFI2)
kl678Hu01 **細胞抗原9(LY9)多克隆抗體 Polyclonal Antibody to Lymphocyte Antigen 9 (LY9)
kl680Mu01 朊病毒蛋白(PRNP)多克隆抗體 Polyclonal Antibody to Prion Protein (PRNP)
kl682Gu01 **球蛋白G2(IgG2)多克隆抗體 Polyclonal Antibody to Immunoglobulin G2 (IgG2)
kl682Hu01 **球蛋白G2(IgG2)多克隆抗體 Polyclonal Antibody to Immunoglobulin G2 (IgG2)
kl683Hu01 Duffy血型趨化因子受體(DARC)多克隆抗體 Polyclonal Antibody to Duffy Blood Group Chemokine Receptor (DARC)
kl684Hu01 細胞因子信號轉導抑制因子3(SOCS3)多克隆抗體 Polyclonal Antibody to Suppressors Of Cytokine Signaling 3 (SOCS3)
kl685Mu01 整合素αM(ITGαM)多克隆抗體 Polyclonal Antibody to Integrin Alpha M (ITGaM)
kl685Ra01 整合素αM(ITGαM)多克隆抗體 Polyclonal Antibody to Integrin Alpha M (ITGaM)
kl686Hu01 B-細胞激活因子(BAFF)多克隆抗體 Polyclonal Antibody to B-Cell Activating Factor (BAFF)
kl686Mu01 B-細胞激活因子(BAFF)多克隆抗體 Polyclonal Antibody to B-Cell Activating Factor (BAFF)
kl686Ra01 B-細胞激活因子(BAFF)多克隆抗體 Polyclonal Antibody to B-Cell Activating Factor (BAFF)
kl688Hu01 白介素21(IL21)多克隆抗體 Polyclonal Antibody to Interleukin 21 (IL21)
kl688Mu01 白介素21(IL21)多克隆抗體 Polyclonal Antibody to Interleukin 21 (IL21)
kl688Ra01 白介素21(IL21)多克隆抗體 Polyclonal Antibody to Interleukin 21 (IL21)
kl689Hu01 白介素28A(IL28A)多克隆抗體 Polyclonal Antibody to Interleukin 28A (IL28A)
kl690Hu01 滲透性糖蛋白(Pgp)多克隆抗體 Polyclonal Antibody to Permeability Glycoprotein (Pgp)

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