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產品詳情
  • 產品名稱:Anti-GMPPB抗體

  • 產品型號:GDP甘露糖焦磷酸化酶B抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-GMPPB抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-GMPPB抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-GMPPB
Cat. Number:
Anti-GMPPB抗體KL-13461R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
GMPPB is a 360 amino acid protein that belongs to the transferase hexapeptide repeat family and is involved in protein modification pathways. Functioning as a GDP-mannose pyrophosphorylase, GMPPB enzymatically catalyzesAnti-GMPPB抗體 the conversion of mannose-1-phosphate and GTP to GDP-mannose and a free phosphate, a reaction that is involved in the production of N-linked oligosaccharides. Defects in the gene encoding GMPPB that cause errors in the glycosylation pathway may lead to congenital disorders of glycosylation (CDG). CDGs are multisystemic diseases that often involve both the central and peripheral nervous systems and are often characterized by endocrine and coagulation disorders. GMPPB is expressed as two isoforms due to alternative splicing events.
Also known as:
GDP mannose pyrophosphorylase B; Anti-GMPPB抗體GDP-mannose pyrophosphorylase B; GMPPB; GMPPB_HUMAN; GTP-mannose-1-phosphate guanylyltransferase beta; KIAA1851; Mannose 1 phosphate guanylyltransferase; Mannose-1-phosphate guanyltransferase beta.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Pig, Cow, Horse, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human GMPPB.
Predicted Molecular Weight: 40kDa.Anti-GMPPB抗體
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   Anti-GMPPB抗體
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.
kl031Ra01 粘蛋白3(MUC3)多克隆抗體 Polyclonal Antibody to Mucin 3 (MUC3)
kl031Bo01 粘蛋白3(MUC3)多克隆抗體 Polyclonal Antibody to Mucin 3 (MUC3)
kl705Hu01 粘蛋白2(MUC2)多克隆抗體 Polyclonal Antibody to Mucin 2 (MUC2)
kl705Mu01 粘蛋白2(MUC2)多克隆抗體 Polyclonal Antibody to Mucin 2 (MUC2)
kl705Ra01 粘蛋白2(MUC2)多克隆抗體 Polyclonal Antibody to Mucin 2 (MUC2)
kl705Bo01 粘蛋白2(MUC2)多克隆抗體 Polyclonal Antibody to Mucin 2 (MUC2)
kl413Hu01 粘蛋白1(MUC1)多克隆抗體 Polyclonal Antibody to Mucin 1 (MUC1)
kl413Mu01 粘蛋白1(MUC1)多克隆抗體 Polyclonal Antibody to Mucin 1 (MUC1)
kl413Ra01 粘蛋白1(MUC1)多克隆抗體 Polyclonal Antibody to Mucin 1 (MUC1)
kl413Bo01 粘蛋白1(MUC1)多克隆抗體 Polyclonal Antibody to Mucin 1 (MUC1)
kl697Hu01 α1-抗胰蛋白酶(α1AT)多克隆抗體 Polyclonal Antibody to Alpha-1-Antitrypsin (a1AT)
kl697Mu01 α1-抗胰蛋白酶(α1AT)多克隆抗體 Polyclonal Antibody to Alpha-1-Antitrypsin (a1AT)
kl697Ra01 α1-抗胰蛋白酶(α1AT)多克隆抗體 Polyclonal Antibody to Alpha-1-Antitrypsin (a1AT)
kl817Hu01 結合珠蛋白(Hpt)多克隆抗體 Polyclonal Antibody to Haptoglobin (Hpt)
kl817Mu01 結合珠蛋白(Hpt)多克隆抗體 Polyclonal Antibody to Haptoglobin (Hpt)
kl817Ra01 結合珠蛋白(Hpt)多克隆抗體 Polyclonal Antibody to Haptoglobin (Hpt)
kl817Gu01 結合珠蛋白(Hpt)多克隆抗體 Polyclonal Antibody to Haptoglobin (Hpt)
kl817Rb53 結合珠蛋白(Hpt)多克隆抗體 Polyclonal Antibody to Haptoglobin (Hpt)
kl236Hu01 纖溶酶原(Plg)多克隆抗體 Polyclonal Antibody to Plasminogen (Plg)
kl236Mu01 纖溶酶原(Plg)多克隆抗體 Polyclonal Antibody to Plasminogen (Plg)
kl236Ra01 纖溶酶原(Plg)多克隆抗體 Polyclonal Antibody to Plasminogen (Plg)
kl017Hu01 α2-巨球蛋白(α2M)多克隆抗體 Polyclonal Antibody to Alpha-2-Macroglobulin (a2M)

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