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產(chǎn)品詳情
  • 產(chǎn)品名稱:Anti-GBA抗體

  • 產(chǎn)品型號:β-葡萄糖腦苷脂酶抗體
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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簡單介紹:
Anti-GBA抗體產(chǎn)品質(zhì)量穩(wěn)定,實驗效果明顯,貨期快,價格優(yōu)惠,歡迎垂詢訂購!我公司長期供應(yīng)**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關(guān)試劑、熒光標(biāo)記抗體、單克隆抗體、多克隆抗體、各種標(biāo)記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-GBA抗體用于**組化實驗,WB實驗,相應(yīng)的標(biāo)記抗體有HRP標(biāo)記抗體,FITC標(biāo)記,BIO等。
詳情介紹:
Rabbit  Anti-GBA
Cat. Number:
Anti-GBA抗體KL-11779R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes a lysosomal membrane protein that cleaves the beta-glucosidic linkage of glycosylceramide, an intermediate in glycolipid metabolism. Mutations in this gene cause Gaucher disease, a lysosomal storage disease Anti-GBA抗體characterized by an accumulation of glucocerebrosides. A related pseudogene is approximately 12 kb downstream of this gene on chromosome 1. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2010]
Also known as:
Glucosidase beta; Acid beta Anti-GBA抗體glucosidase; Acid beta-glucosidase; Alglucerase; Beta glucocerebrosidase; BETA GLUCOSIDASE, ACID; Beta-glucocerebrosidase; betaGC; D glucosyl N acylsphingosine glucohydrolase; D-glucosyl-N-acylsphingosine glucohydrolase; EC 3.2.1.45 ; GBA; Gba protein; GBA1; GC antibody GCase; GCB; GLCM_HUMAN; GLUC; Glucocerebrosidase (alt.); Glucocerebrosidase; GLUCOCEREBROSIDASE PSEUDOGENE; Glucosidase beta; Glucosidase, beta, acid; Glucosidase, beta; acid (includes glucosylceramidase); Glucosylceramidase; Imiglucerase; Lysosomal glucocerebrosidase.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Rabbit, .Anti-GBA抗體
Immunogen: KLH conjugated synthetic peptide derived from human Glucosid.
Predicted Molecular Weight: 56kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   Anti-GBA抗體
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.
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kl077Hu01 層粘連蛋白α4(LAMα4)多克隆抗體 Polyclonal Antibody to Laminin Alpha 4 (LAMa4)
kl078Hu01 層粘連蛋白α5(LAMα5)多克隆抗體 Polyclonal Antibody to Laminin Alpha 5 (LAMa5)
kl080Hu01 層粘連蛋白β2(LAMβ2)多克隆抗體 Polyclonal Antibody to Laminin Beta 2 (LAMb2)
kl081Hu01 層粘連蛋白β3(LAMβ3)多克隆抗體 Polyclonal Antibody to Laminin Beta 3 (LAMb3)
kl083Hu01 層粘連蛋白γ2(LAMγ2)多克隆抗體 Polyclonal Antibody to Laminin Gamma 2 (LAMC2)
kl086Hu01 Ⅰ類主要組織相容性復(fù)合體C(MHCC)多克隆抗體 Polyclonal Antibody to Major Histocomklibility Complex Class I C (MHCC)
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kl105Mu01 骨形成蛋白8B(BMP8B)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 8B (BMP8B)
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kl107Hu01 骨形成蛋白15(BMP15)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 15 (BMP15)
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kl109Ra01 生長分化因子3(GDF3)多克隆抗體 Polyclonal Antibody to Growth Differentiation Factor 3 (GDF3)

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