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產(chǎn)品詳情
  • 產(chǎn)品名稱:Anti-Fukutin抗體

  • 產(chǎn)品型號:巖藻糖變旋酶/Fucose mutarotase抗體
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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簡單介紹:
Anti-Fukutin抗體產(chǎn)品質(zhì)量穩(wěn)定,實驗效果明顯,貨期快,價格優(yōu)惠,歡迎垂詢訂購!我公司長期供應(yīng)**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關(guān)試劑、熒光標(biāo)記抗體、單克隆抗體、多克隆抗體、各種標(biāo)記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-Fukutin抗體用于**組化實驗,WB實驗,相應(yīng)的標(biāo)記抗體有HRP標(biāo)記抗體,FITC標(biāo)記,BIO等。
詳情介紹:
Rabbit  Anti-Fukutin
Cat. Number:
Anti-Fukutin抗體KL-13226R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Fukutin, a secreted protein, is expressed in various tissues in normal individuals. Fukutin colocalizes with a Golgi marker and a granular cytoplasmic distribution, suggesting that fukutin passes through the Golgi before being packagedAnti-Fukutin抗體 into secretory vesicles. Fukutin may be located in the extracellular matrix, where it interacts with and reinforces a large complex encompassing the outside and inside of muscle membranes; alternatively, as a secreted protein, fukutin may cause muscular dystrophy by an unknown mechanism. The fukutin gene is expressed at similar levels in control fetal and ***** brain, but is much reduced in Fukuyama congenital muscular dystrophy (FCMD) brains. Fukutin deficiency affects the modification of glycosylation of DAG1 (α-dystroglycan), which then cannot localize or function properly and may be degraded or eluted from the extracellular surface membrane of the muscle fiber. FCMD is the first human disease known to be caused by an ancient retrotransposal integration. The gene which encodes fukutin maps to human chromosome 9q31.
Also known as:
C10orf125; Chromosome Anti-Fukutin抗體10 open reading frame 125; FUCM_HUMAN; Fucose mutarotase; FUCU; Protein fucU homolog.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse,Anti-Fukutin抗體 Rat, Dog, Pig, Cow, .
Immunogen: KLH conjugated synthetic peptide derived from human Fukutin.
Predicted Molecular Weight: 17kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-Fukutin抗體
Optimal working dilutions must be determined by the end user.
kl394Ra01 組織因子通道抑制因子(TFPI)多克隆抗體 Polyclonal Antibody to Tissue Factor klhway Inhibitor (TFPI)
kl394Rb51 組織因子通道抑制因子(TFPI)多克隆抗體 Polyclonal Antibody to Tissue Factor klhway Inhibitor (TFPI)
kl395Hu01 抑制素A(INHA)多克隆抗體 Polyclonal Antibody to Inhibin A (INHA)
kl395Po01 抑制素A(INHA)多克隆抗體 Polyclonal Antibody to Inhibin A (INHA)
kl395Ra01 抑制素A(INHA)多克隆抗體 Polyclonal Antibody to Inhibin A (INHA)
kl396Hu01 性**結(jié)合球蛋白(SHBG)多克隆抗體 Polyclonal Antibody to Sex Hormone Binding Globulin (SHBG)
kl396Mu01 性**結(jié)合球蛋白(SHBG)多克隆抗體 Polyclonal Antibody to Sex Hormone Binding Globulin (SHBG)
kl396Ra01 性**結(jié)合球蛋白(SHBG)多克隆抗體 Polyclonal Antibody to Sex Hormone Binding Globulin (SHBG)
kl397Hu01 轉(zhuǎn)化生長因子β受體Ⅰ(TGFβR1)多克隆抗體 Polyclonal Antibody to Transforming Growth Factor Beta Receptor I (TGFbR1)
kl399Ca01 高遷移率族蛋白1(HMG1)多克隆抗體 Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)
kl399Hu01 高遷移率族蛋白1(HMG1)多克隆抗體 Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)
kl399Mu01 高遷移率族蛋白1(HMG1)多克隆抗體 Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)
kl399Po01 高遷移率族蛋白1(HMG1)多克隆抗體 Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)
kl399Ra01 高遷移率族蛋白1(HMG1)多克隆抗體 Polyclonal Antibody to High Mobility Group Protein 1 (HMG1)
kl402Hu01 基質(zhì)金屬蛋白酶12(MMP12)多克隆抗體 Polyclonal Antibody to Matrix Metalloproteinase 12 (MMP12)
kl402Mu01 基質(zhì)金屬蛋白酶12(MMP12)多克隆抗體 Polyclonal Antibody to Matrix Metalloproteinase 12 (MMP12)
kl402Ra01 基質(zhì)金屬蛋白酶12(MMP12)多克隆抗體 Polyclonal Antibody to Matrix Metalloproteinase 12 (MMP12)

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