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產品詳情
  • 產品名稱:Anti-EVC1抗體

  • 產品型號:軟骨外胚層發育**相關蛋白抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-EVC1抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-EVC1抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-EVC1
Cat. Number:
Anti-EVC1抗體KL-11282R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
EVC is an autosomal skeletal dysplasia caused by mutations in the EVC and EVC2 genes. Found in developing ribs, heart, kidney and lung, the EVC gene is responsible for normal development of the face, limbs, teeth and nails. Anti-EVC1抗體The protein expressed by the EVC gene is an intracellular component of the hedgehog signal pathway that contains a leucine zipper and transmembrane domain. Defects in the EVC gene can lead to short-limb dwarfism, ectodermal dysplasia and cardiac anomalies such as irregular atrioventricular septum development. Additionally, the EVC gene has been implicated in Weyers acrodental dysostosis, an autosomal dominant disease characterized by facial abnormalities and limb defects.
Also known as:
Ellis van Creveld syndrome DWF 1; Anti-EVC1抗體DWF1; Ellis van Creveld syndrome protein; Ellis-van Creveld syndrome; EVC; EVC1; EVC 1; EVC-1; EVCL; MGC105107; EVC_HUMAN.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, .
Immunogen: KLH conjugated synthetic peptide derived from human EVC1.
Predicted Molecular Weight:Anti-EVC1抗體 112kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-EVC1抗體
Optimal working dilutions must be determined by the end user.
kl129Hu01 組織金屬蛋白酶抑制因子3(TIMP3)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 3 (TIMP3)
kl129Mu01 組織金屬蛋白酶抑制因子3(TIMP3)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 3 (TIMP3)
kl129Po01 組織金屬蛋白酶抑制因子3(TIMP3)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 3 (TIMP3)
kl129Ra01 組織金屬蛋白酶抑制因子3(TIMP3)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 3 (TIMP3)
kl129Rb51 組織金屬蛋白酶抑制因子3(TIMP3)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 3 (TIMP3)
kl129Si01 組織金屬蛋白酶抑制因子3(TIMP3)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 3 (TIMP3)
kl130Bo01 組織金屬蛋白酶抑制因子4(TIMP4)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 4 (TIMP4)
kl130Hu01 組織金屬蛋白酶抑制因子4(TIMP4)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 4 (TIMP4)
kl130Mu01 組織金屬蛋白酶抑制因子4(TIMP4)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 4 (TIMP4)
kl130Po01 組織金屬蛋白酶抑制因子4(TIMP4)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 4 (TIMP4)
kl130Ra01 組織金屬蛋白酶抑制因子4(TIMP4)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 4 (TIMP4)
kl130Rb51 組織金屬蛋白酶抑制因子4(TIMP4)多克隆抗體 Polyclonal Antibody to Tissue Inhibitors Of Metalloproteinase 4 (TIMP4)
kl131Bo01 轉化生長因子β誘導蛋白(TGFβI)多克隆抗體 Polyclonal Antibody to Transforming Growth Factor Beta Induced Protein (TGFbI)
kl131Fi01 轉化生長因子β誘導蛋白(TGFβI)多克隆抗體 Polyclonal Antibody to Transforming Growth Factor Beta Induced Protein (TGFbI)
kl131Hu01 轉化生長因子β誘導蛋白(TGFβI)多克隆抗體 Polyclonal Antibody to Transforming Growth Factor Beta Induced Protein (TGFbI)
kl131Mu01 轉化生長因子β誘導蛋白(TGFβI)多克隆抗體 Polyclonal Antibody to Transforming Growth Factor Beta Induced Protein (TGFbI)

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