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產(chǎn)品詳情
  • 產(chǎn)品名稱:Anti-ETHE1抗體

  • 產(chǎn)品型號:乙基丙二酸腦病蛋白抗體
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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簡單介紹:
Anti-ETHE1抗體產(chǎn)品質(zhì)量穩(wěn)定,實(shí)驗(yàn)效果明顯,貨期快,價格優(yōu)惠,歡迎垂詢訂購!我公司長期供應(yīng)**組化抗體、WB抗體、**組化試劑盒和抗體試驗(yàn)所需全部相關(guān)試劑、熒光標(biāo)記抗體、單克隆抗體、多克隆抗體、各種標(biāo)記的二抗IgG/IgM/IgD/IgA等科研實(shí)驗(yàn)抗體。Anti-ETHE1抗體用于**組化實(shí)驗(yàn),WB實(shí)驗(yàn),相應(yīng)的標(biāo)記抗體有HRP標(biāo)記抗體,FITC標(biāo)記,BIO等。
詳情介紹:
Rabbit  Anti-ETHE1
Cat. Number:
Anti-ETHE1抗體KL-7610R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Probably plays an important role in metabolic homeostasis in mitochondria. May function as a nuclear-cytoplasmic shuttling Anti-ETHE1抗體protein that binds transcription factor RELA/NFKB3 in the nucleus and exports it to the cytoplasm. Suppresses p53-induced apoptosis by preventing nuclear localization of RELA.
Involvement in disease:Defects in ETHE1 are a cause of ethylmalonic encephalopathy (EE) . EE is an autosomal recessive disorder characterized by neurodevelopmental delay and regression, recurrent petechiae, acrocyanosis,Anti-ETHE1抗體 diarrhea, leading to death in the first decade of life. It is also associated with persistent lactic acidemia and ethylmalonic and methylsuccinic aciduria.
Also known as:
mitochondrial; Ethe1; ETHE1 Anti-ETHE1抗體protein, mitochondrial precursor; ETHE1_HUMAN; ethylmalonic encephalopathy 1; Ethylmalonic encephalopathy protein 1; hepatoma subtracted clone one; Hepatoma subtracted clone one protein; HSCO; Protein ETHE1; YF13H12.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Dog, Pig, Cow, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human ETHE1.
Predicted Molecular Weight: 26kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-ETHE1抗體
Optimal working dilutions must be determined by the end user.
kl215Hu01 中心體肌動蛋白β(CTRN2)多克隆抗體 Polyclonal Antibody to Centractin Beta (CTRN2)
kl215Mu01 中心體肌動蛋白β(CTRN2)多克隆抗體 Polyclonal Antibody to Centractin Beta (CTRN2)
kl215Ra01 中心體肌動蛋白β(CTRN2)多克隆抗體 Polyclonal Antibody to Centractin Beta (CTRN2)
kl297Hu01 核糖核酸酶A(RNASE1)多克隆抗體 Polyclonal Antibody to Ribonuclease A (RNASE1)
kl762Hu01 磷酸化酶激酶β(PHKβ)多克隆抗體 Polyclonal Antibody to Phosphorylase Kinase Beta (PHKb)
kl762Mu01 磷酸化酶激酶β(PHKβ)多克隆抗體 Polyclonal Antibody to Phosphorylase Kinase Beta (PHKb)
kl762Ra01 磷酸化酶激酶β(PHKβ)多克隆抗體 Polyclonal Antibody to Phosphorylase Kinase Beta (PHKb)
kl178Hu01 α2-HS糖蛋白(αHSG)多克隆抗體 Polyclonal Antibody to Alpha-2-Heremans Schmid Glycoprotein (aHSG)
kl178Mu01 α2-HS糖蛋白(αHSG)多克隆抗體 Polyclonal Antibody to Alpha-2-Heremans Schmid Glycoprotein (aHSG)
kl178Ra01 α2-HS糖蛋白(αHSG)多克隆抗體 Polyclonal Antibody to Alpha-2-Heremans Schmid Glycoprotein (aHSG)
kl545Hu01 **球蛋白E(IgE)多克隆抗體 Polyclonal Antibody to Immunoglobulin E (IgE)
kl545Mu01 **球蛋白E(IgE)多克隆抗體 Polyclonal Antibody to Immunoglobulin E (IgE)
kl545Ra01 **球蛋白E(IgE)多克隆抗體 Polyclonal Antibody to Immunoglobulin E (IgE)
kl436Hu01 肌球蛋白ⅠG(MYO1G)多克隆抗體 Polyclonal Antibody to Myosin IG (MYO1G)
kl436Mu01 肌球蛋白ⅠG(MYO1G)多克隆抗體 Polyclonal Antibody to Myosin IG (MYO1G)
kl436Ra01 肌球蛋白ⅠG(MYO1G)多克隆抗體 Polyclonal Antibody to Myosin IG (MYO1G)
kl435Hu01 肌球蛋白ⅠF(MYO1F)多克隆抗體 Polyclonal Antibody to Myosin IF (MYO1F)
kl435Mu01 肌球蛋白ⅠF(MYO1F)多克隆抗體 Polyclonal Antibody to Myosin IF (MYO1F)
kl435Ra01 肌球蛋白ⅠF(MYO1F)多克隆抗體 Polyclonal Antibody to Myosin IF (MYO1F)

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