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產品詳情
  • 產品名稱:Anti-EVC2抗體

  • 產品型號:膜蛋白EVC2抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-EVC2抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-EVC2抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-EVC2
Cat. Number:
Anti-EVC2抗體KL-6638R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
EVC2 is an integralAnti-EVC2抗體 membrane protein that plays a vital role in bone formation and skeletal development. Defects in EVC2 are a cause of Ellis-van Creveld syndrome (EVC), also known as chondroectodermal dysplasia. EVC is an autosomal recessive disorder characterized by the clinical tetrad of chondrodystrophy, polydactyly, ectodermal dysplasia and cardiac anomalies. Patients manifest short-limb dwarfism, short ribs, postaxial polydactyly and dysplastic nails and teeth. Congenital heart defects, most commonly an atrioventricular septal defect, are observed in 60% of affected individuals.
Also known as:
Ellis van Creveld syndrome 2; Anti-EVC2抗體LBN; Limbin; LBN_HUMAN.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, .
Immunogen: KLH conjugated synthetic peptide derived from human EVC2 (11.
Predicted Molecular Weight: Anti-EVC2抗體145kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   Anti-EVC2抗體
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.
kl042Ra01 法尼酯X受體(FXR)多克隆抗體 Polyclonal Antibody to Farnesoid X Receptor (FXR)
kl043Hu01 維甲酸X受體α(RXRα)多克隆抗體 Polyclonal Antibody to Retinoid X Receptor Alpha (RXRa)
kl043Mu01 維甲酸X受體α(RXRα)多克隆抗體 Polyclonal Antibody to Retinoid X Receptor Alpha (RXRa)
kl043Mu02 維甲酸X受體α(RXRα)多克隆抗體 Polyclonal Antibody to Retinoid X Receptor Alpha (RXRa)
kl044Mu01 肝X受體α(LXRα)多克隆抗體 Polyclonal Antibody to Liver X Receptor Alpha (LXRa)
kl044Mu02 肝X受體α(LXRα)多克隆抗體 Polyclonal Antibody to Liver X Receptor Alpha (LXRa)
kl045Mu02 存活素(Surv)多克隆抗體 Polyclonal Antibody to Survivin (Surv)
kl046Mu01 S100鈣結合蛋白A10(S100A10)多克隆抗體 Polyclonal Antibody to S100 Calcium Binding Protein A10 (S100A10)
kl046Mu02 S100鈣結合蛋白A10(S100A10)多克隆抗體 Polyclonal Antibody to S100 Calcium Binding Protein A10 (S100A10)
kl047Mu02 Ki-67蛋白(Ki67P)多克隆抗體 Polyclonal Antibody to Ki-67 Protein (Ki67P)
kl056Mu02 基質金屬蛋白酶14(MMP14)多克隆抗體 Polyclonal Antibody to Matrix Metalloproteinase 14 (MMP14)
kl058Mu01 白介素20(IL20)多克隆抗體 Polyclonal Antibody to Interleukin 20 (IL20)
kl058Mu02 白介素20(IL20)多克隆抗體 Polyclonal Antibody to Interleukin 20 (IL20)
kl058Ra01 白介素20(IL20)多克隆抗體 Polyclonal Antibody to Interleukin 20 (IL20)
kl059Hu01 周期素依賴性激酶6(CDK6)多克隆抗體 Polyclonal Antibody to Cyclin Dependent Kinase 6 (CDK6)

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