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產品詳情
  • 產品名稱:Anti-BBS10抗體

  • 產品型號:巴爾得-別德爾綜合征相關蛋白10抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-BBS10抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-BBS10抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-BBS10
Cat. Number:
Anti-BBS10抗體KL-11512R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Bardet-Biedl syndrome Anti-BBS10抗體(BBS) is a pleiotropic genetic disorder characterized by obesity, photoreceptor degeneration, polydactyly, hypogenitalism, renal abnormalities, and developmental delay. Other associated clinical findings in BBS patients include diabetes, hypertension, and congenital heart defects. BBS genes map to multiple loci and encode fourteen proteins, BBS1-BBS14. Many BBS genes encode basal body or cilia proteins, suggesting that BBS is a ciliary dysfunction disorder. BBS10 (Bardet-Biedl syndrome 10), also known as chromosome 12 open reading fame 58, C12orf58 or FLJ23560, is a novel 723 amino acid protein belonging to the TCP-1 chaperonin family. BBS10 localizes to the basal body of primary cilium and assists in protein folding upon ATP hydrolysis. Inhibition of BBS10 has been found to impair ciliogenesis, activate the glycogen synthase kinase 3 pathway and cause peroxisome proliferator-activated receptor nuclear accumulation. The gene encoding BBS10 contains two exons and maps to human chromosome 12q21.2.Anti-BBS10抗體
Also known as:
Bardet Biedl syndrome 10 protein; Bardet Biedl syndrome 10 protein homolog; C12orf58; FLJ23560; RGD1560748; BBS10_HUMAN.Anti-BBS10抗體
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, .
Immunogen: KLH conjugated synthetic peptide derived from human BBS10.
Predicted Molecular Weight: 81kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working Anti-BBS10抗體dilutions must be determined by the end user.
kl537Ra01 神經元特異性烯醇化酶(NSE)多克隆抗體 Polyclonal Antibody to Enolase, Neuron Specific (NSE)
kl547Hu01 血管細胞粘附分子1(VCAM1)多克隆抗體 Polyclonal Antibody to Vascular Cell Adhesion Molecule 1 (VCAM1)
kl547Mu01 血管細胞粘附分子1(VCAM1)多克隆抗體 Polyclonal Antibody to Vascular Cell Adhesion Molecule 1 (VCAM1)
kl547Ra01 血管細胞粘附分子1(VCAM1)多克隆抗體 Polyclonal Antibody to Vascular Cell Adhesion Molecule 1 (VCAM1)
kl547Rb52 血管細胞粘附分子1(VCAM1)多克隆抗體 Polyclonal Antibody to Vascular Cell Adhesion Molecule 1 (VCAM1)
kl547Si01 血管細胞粘附分子1(VCAM1)多克隆抗體 Polyclonal Antibody to Vascular Cell Adhesion Molecule 1 (VCAM1)
kl548Ca01 細胞間粘附分子1(ICAM1)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 1 (ICAM1)
kl548Hu01 細胞間粘附分子1(ICAM1)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 1 (ICAM1)
kl548Mu01 細胞間粘附分子1(ICAM1)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 1 (ICAM1)
kl548Po01 細胞間粘附分子1(ICAM1)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 1 (ICAM1)
kl548Ra01 細胞間粘附分子1(ICAM1)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 1 (ICAM1)
kl548Rb51 細胞間粘附分子1(ICAM1)多克隆抗體 Polyclonal Antibody to Intercellular Adhesion Molecule 1 (ICAM1)
kl549Hu01 角蛋白9(KRT9)多克隆抗體 Polyclonal Antibody to Keratin 9 (KRT9)
kl549Mu01 角蛋白9(KRT9)多克隆抗體 Polyclonal Antibody to Keratin 9 (KRT9)
kl551Bo01 堿性成纖維細胞生長因子(FGF2)多克隆抗體 Polyclonal Antibody to Fibroblast Growth Factor 2, Basic (FGF2)
kl551Ga01 堿性成纖維細胞生長因子(FGF2)多克隆抗體 Polyclonal Antibody to Fibroblast Growth Factor 2, Basic (FGF2)

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